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HPS1 Rabbit anti-Human, Polyclonal, Proteintech
Rabbit Polyclonal Antibody
Marke: Proteintech 15077-1-AP-20UL
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Beschreibung
Hermansky-Pudlak syndrome (HPS) is a rare, genetically heterogeneous, autosomal recessive disorder. It is characterized by oculocutaneous albinism, lysosomal storage defects and prolonged bleeding due to platelet storage pool deficiency. There are 10 HPS genes encoding HPS proteins that all interact within three distinct ubiquitously expressed protein complexes or biogenesis of lysosome-related organelle complexes. Defects in these genes cause HPS. HSP-1 is a component of multiple cytoplasmic organelles and is important for their normal development and function. It plays a role in intracellular protein sorting.Spezifikation
HPS1 | |
Polyclonal | |
Unconjugated | |
HPS1 | |
Hermansky Pudlak syndrome 1, HPS, HPS1 | |
Rabbit | |
Antigen Affinity Chromatography | |
RUO | |
3257 | |
-20°C | |
Liquid |
Immunofluorescence, Immunocytochemistry, Western Blot | |
0.24 mg/mL | |
PBS with 50% glycerol and 0.02% sodium azide; pH 7.3 | |
Q92902 | |
HPS1 | |
HPS1 Fusion Protein Ag7149 | |
20 μL | |
Primary | |
Human | |
Antibody | |
IgG |
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